A rosette-forming glioneuronal tumour (RGNT) is a rare tumour with new information emerging. We review the literature and describe the second patient with a RGNT arising from the pineal gland. This is also the fifth report of a RGNT arising from outside the fourth ventricle. The prognosis of RGNT remains guarded, as long-term follow-up is not yet available for most patients reported. With only one of 35 patients having a documented recurrence at 10 years, the prognosis seems favourable with appropriate, but not necessarily total, surgical resection.
- Fourth ventricle
- Low-grade CNS tumour
- Pilocytic astrocytoma
- Rosette-forming glioneuronal tumour