Abstract
Osteogenesis imperfecta (OI) is a disorder of bone development caused by a genetic dysfunction of collagen synthesis. Basilar invagination (BI) is an uncommon but serious complication of OI. Brainstem decompression in OI is undertaken in certain circumstances. Transoral-transpalatopharyngeal ventral decompression with posterior occipitocervical fusion has become the treatment of choice when required. This technical note Outlines a novel endoscopic transnasal approach for ventral decompression. The literature is reviewed and a strategy for the management of BI in patients with OI is Outlined.
Original language | English |
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Pages (from-to) | 354-357 |
Number of pages | 4 |
Journal | Journal of Neurosurgery: Spine |
Volume | 9 |
Issue number | 4 |
DOIs | |
Publication status | Published - Oct 2008 |
Externally published | Yes |
Keywords
- basilar invagination
- occipitocervical fusion
- odontoidectomy
- osteogenesis imperfecta
- transnasal approach
- IMPRESSION