Large internal auditory meatus, inner ear anomalies, and progressive hearing loss

The present paper describes a case demonstrating an abnormality of a large internal auditory meatus (LIAM) together with other inner ear anomalies. The otic capsule was affected by a widened, bulbar internal auditory meatus with loss of the bony wall dividing the lateral end of the meatus from the cochlea. The vestible was also abnormally dilated. The child suffered a progressive loss of cochlear function with apparent fluctuation of hearing and some episodes of sudden hearing loss.