Multiple complications of advanced IPF in an individual patient presentation

Thomas Ledger; Stanley Braude

doi:10.1002/rcr2.1118

Multiple complications of advanced IPF in an individual patient presentation

Research output: Contribution to journal › Article › peer-review

Abstract

We report a patient with advanced idiopathic pulmonary fibrosis (IPF), who in a single presentation experienced three complications of the disease: an acute exacerbation, spontaneous pneumomediastinum, and platypnoea-orthodeoxia syndrome. Despite there being no definitive evidence-based treatment for an acute exacerbation, we report a marked improvement with high-dose steroids. This case also highlights the importance in IPF patients of considering pneumomediastinum as a cause of non-cardiac chest pain, as well as platypnoea-orthodeoxia in those with positional dyspnoea.

Original language	English
Article number	e01118
Pages (from-to)	1-3
Number of pages	3
Journal	Respirology Case Reports
Volume	11
Issue number	4
DOIs	https://doi.org/10.1002/rcr2.1118
Publication status	Published - Apr 2023
Externally published	Yes

Bibliographical note

Copyright the Author(s) 2023. Version archived for private and non-commercial use with the permission of the author/s and according to publisher conditions. For further rights please contact the publisher.

Keywords

acute exacerbation of idiopathic pulmonary fibrosis
idiopathic pulmonary fibrosis
platypnoea-orthodeoxia syndrome
pneumomediastinum

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10.1002/rcr2.1118Licence: CC BY-NC-ND

Publisher version (open access)Final published version, 448 KBLicence: CC BY-NC-ND

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abstract = "We report a patient with advanced idiopathic pulmonary fibrosis (IPF), who in a single presentation experienced three complications of the disease: an acute exacerbation, spontaneous pneumomediastinum, and platypnoea-orthodeoxia syndrome. Despite there being no definitive evidence-based treatment for an acute exacerbation, we report a marked improvement with high-dose steroids. This case also highlights the importance in IPF patients of considering pneumomediastinum as a cause of non-cardiac chest pain, as well as platypnoea-orthodeoxia in those with positional dyspnoea. ",

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AU - Braude, Stanley

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N2 - We report a patient with advanced idiopathic pulmonary fibrosis (IPF), who in a single presentation experienced three complications of the disease: an acute exacerbation, spontaneous pneumomediastinum, and platypnoea-orthodeoxia syndrome. Despite there being no definitive evidence-based treatment for an acute exacerbation, we report a marked improvement with high-dose steroids. This case also highlights the importance in IPF patients of considering pneumomediastinum as a cause of non-cardiac chest pain, as well as platypnoea-orthodeoxia in those with positional dyspnoea.

AB - We report a patient with advanced idiopathic pulmonary fibrosis (IPF), who in a single presentation experienced three complications of the disease: an acute exacerbation, spontaneous pneumomediastinum, and platypnoea-orthodeoxia syndrome. Despite there being no definitive evidence-based treatment for an acute exacerbation, we report a marked improvement with high-dose steroids. This case also highlights the importance in IPF patients of considering pneumomediastinum as a cause of non-cardiac chest pain, as well as platypnoea-orthodeoxia in those with positional dyspnoea.

KW - acute exacerbation of idiopathic pulmonary fibrosis

KW - idiopathic pulmonary fibrosis

KW - platypnoea-orthodeoxia syndrome

KW - pneumomediastinum

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JO - Respirology Case Reports

JF - Respirology Case Reports

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ER -

Multiple complications of advanced IPF in an individual patient presentation

Abstract

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Keywords

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