Noncraniofacial manifestations of crouzon’s disease

Timothy W. Proudman*, Mark H. Moore, Amanda H. Abbott, David J. David

*Corresponding author for this work

Research output: Contribution to journalArticlepeer-review

28 Citations (Scopus)


Although most interest centers on the craniofacial region in Crouzon’s disease, noncraniofacial manifestations are important because they may complicate both diagnosis and management. A population of 59 patients with Crouzon’s disease was reviewed to determine the frequency of these deformities. Sty-lohyoid ligament calcification (50%) and cervical spine (40%) and elbow (18%) abnormalities were the most common. Minor hand deformities (10%), other musculoskeletal deformities (7%), and visceral anomalies (7%) were also seen. Acanthosis nigricans was not present in this population. Recommendations are made for the assessment and management of Crouzon’s disease with reference to these areas.

Original languageEnglish
Pages (from-to)218-222
Number of pages5
JournalJournal of Craniofacial Surgery
Issue number4
Publication statusPublished - 1994
Externally publishedYes


  • Craniofacial dysostosis
  • Noncraniofacial abnormalities


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