Recapitulation of skewed X-inactivation in female ornithine transcarbamylase-deficient primary human hepatocytes in the FRG mouse: a novel system for developing epigenetic therapies

Sharon C. Cunningham, Eva B. Van Dijk, Erhua Zhu, Maya Sugden, Mawj Mandwie, Susan Siew, Beena Devanapalli, Adviye Ayper Tolun, Anne Klein, Laurence Wilson, Nader Aryamanesh, Paul Gissen, Julien Baruteau, Kaustuv Bhattacharya, Ian E. Alexander^*