Recurrent pyogenic cholangitis or 'oriental cholangiohepatitis' in occidentals: Case reports of four patients

The first description of recurrent pyogenic cholangitis occurring in four occidentals is presented. While recurrent pyogenic cholangitis is a common syndrome of uncertain aetiology among orientals (also known as oriental cholangiohepatitis), it has not previously been described in occidentals. Four such patients are described. They presented with recurrent attacks of ascending cholangitis and associated hepatolithiasis, biliary stricturing and dilatation. Focal hepatic involvement was treated by segmental liver resection and recurrent disease by interventional endoscopy or radiology.