Surgical correction of crouzon syndrome

David J. David*, Robert Sheen

*Corresponding author for this work

Research output: Contribution to journalArticlepeer-review

41 Citations (Scopus)

Abstract

This study analyzes the results of surgical treatment in 39 patients with the Crouzon syndrome. Early fronto-orbital advancement and craniectomy were universally successful in relieving raised intracranial pressure and in reducing ocular proptosis. However, definitive cosmetic correction was not achieved, and early cranial surgery was not able to prevent the development of midface hypoplasia. Thirty-two midfacial advancements have been performed in 39 patients. Sixteen patients had sufficient follow-up data for more than 2 years postoperatively. In all patients, a satisfactory early postoperative result was achieved. In the long-term follow-up group, 11 patients have maintained a satisfactory appearance, while 5 have developed recurrent deformity. Analysis shows this to be associated with a younger age at operation and continued mandibular growth. Erontofacial advancement in adults achieves good long-term results but is associated with a higher incidence of complications.

Original languageEnglish
Pages (from-to)344-354
Number of pages11
JournalPlastic and Reconstructive Surgery
Volume85
Issue number3
Publication statusPublished - 1990
Externally publishedYes

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