Abstract
A 71-year-old man was referred to neuro-ophthalmology for evaluation of reading problems associated with pituitary adenoma. Perimetry showed a right temporal crescent syndrome (“half moon” syndrome) suggesting left occipital disease. Cranial magnetic resonance imaging, electroencephalogram, and cerebrospinal fluid examination (14-3-3 protein) were consistent with a diagnosis of Creutzfeldt-Jakob disease. His neurologic condition rapidly deteriorated with memory problems, myoclonus, and apathy followed by death, 4 months later. This case shows how visual problems may be the first manifestation of this rare prion disease (Heidenhain variant of Creutzfeldt-Jakob disease).
Original language | English |
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Pages (from-to) | 381-385 |
Number of pages | 5 |
Journal | Survey of Ophthalmology |
Volume | 65 |
Issue number | 3 |
DOIs | |
Publication status | Published - 1 May 2020 |
Externally published | Yes |
Keywords
- half moon syndrome
- Heidenhain variant of Creutzfeldt-Jakob disease
- temporal crescent syndrome